Relevance. Pulmonary sequestrations are rare pathology and make from 0.15 to 6.4 % of all congenital abnormality. Thus intra-abdominal localization of this malformation is described only in 2.5 % of all pulmonary sequestrations. Objective. Reflect the difficulty of differential diagnosis of rare lung malformation in newborns. Materials and methods. 2 cases of the extralobar sequestration located under the diaphragm diagnosed for newborns in a children's hospital for the last 20 years are in details described. Results. The diagnosis of an intra-abdominal extralobular pulmonary sequestration was finalized only after surgical treatment, confirmed histologically. Questions of differential diagnostics of rare congenital pulmonary malformations are discussed with tumors of suprarenal localization at newborns, comparison of own results to data of literature. Conclusions. In the differential diagnosis of suprarenal lesions at newborns it is necessary to consider the possibility of intra-abdominal extralobar pulmonary sequestration, especially in the localization of pathological changes at the left side.